Malignant Extragastrointestinal Neuroectodermal Tumor Located at Right Cervical Region

Nil Çomunoğlu¹, Sergülen Dervişoğlu¹, Bilge Başkır Elçin¹, Gonca Ayşe Tekant², Hilmi Apak³

¹Department of Pathology, Cerrahpasa Faculty of Medicine, Istanbul University, Istanbul, Turkey.
²Department of Pediatric Surgery, Cerrahpasa Faculty of Medicine, Istanbul University, Istanbul, Turkey.
³Department of Pediatric Hematooncology, Cerrahpasa Faculty of Medicine, Istanbul University, Istanbul, Turkey.

DOI: 10.4236/ojpathology.2015.54017                

Abstract

Malignant Gastrointestinal Neuroectodermal Tumor (GNET) is a recently described rare malignant neoplasm, resembling “clear cell sarcoma of tendons and aponeuroses” morphologically, immunohistochemically and molecular pathologically. We will describe a case of soft tissue sarcoma located at right cervical region of a 9-year-old male patient, mimicking malignant GNET, which can be considered as extragastrointestinal counterpart of this tumor. These tumors have poor prognosis. This is unique, possibly the first case of a soft tissue sarcoma resembling GNET.

Keywords

Gastrointestinal Neuroectodermal Tumor, Clear Cell Sarcoma, S-100 Protein

Conflicts of Interest

The authors declare no conflicts of interest.

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