TITLE:
Malignant Extragastrointestinal Neuroectodermal Tumor Located at Right Cervical Region
AUTHORS:
Nil Çomunoğlu, Sergülen Dervişoğlu, Bilge Başkır Elçin, Gonca Ayşe Tekant, Hilmi Apak
KEYWORDS:
Gastrointestinal Neuroectodermal Tumor, Clear Cell Sarcoma, S-100 Protein
JOURNAL NAME:
Open Journal of Pathology,
Vol.5 No.4,
October
16,
2015
ABSTRACT: Malignant Gastrointestinal Neuroectodermal
Tumor (GNET) is a recently described rare malignant neoplasm, resembling “clear
cell sarcoma of tendons and aponeuroses” morphologically,
immunohistochemically and molecular pathologically. We will describe a case of
soft tissue sarcoma located at right cervical region of a 9-year-old male
patient, mimicking malignant GNET, which can be considered as
extragastrointestinal counterpart of this tumor. These tumors have poor
prognosis. This is unique, possibly the first case of a soft tissue sarcoma
resembling GNET.