Kimura’s Disease—A Rare Cause of Head and Neck Swelling


Kimura’s disease (KD) is a chronic inflammatory disorder with unknown etiology, most commonly manifesting as painless unilateral cervical lymphadenopathy or subcutaneous masses in the head or neck region. The disease is characterized by a triad of painless subcutaneous masses in the head or neck region, blood and tissue eosinophilia, and markedly elevated serum immunoglobulin E levels. Kimura’s disease is an unusual vascular tumor that typically occurs at 20 to 30 years of age. There has been no documented case of malignant transformation; however, recurrence rates after excision may be as high as 25%. Surgery and medical therapy are useful for treatment. We present a 14 years old male developed a unilateral cervical mass associated with KD. It was a recurrence of disease. As a complete excisional resection of the mass already done 1 year back at some other centre, we decided to give medical treatment for Kimura’s disease.

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Rao, K. and Kumar, S. (2014) Kimura’s Disease—A Rare Cause of Head and Neck Swelling. International Journal of Otolaryngology and Head & Neck Surgery, 3, 200-204. doi: 10.4236/ijohns.2014.34037.

Conflicts of Interest

The authors declare no conflicts of interest.


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