TITLE:
A Rare Case of Apple-Peel Configuration of the Small Intestine Associated with Intestinal Malrotation
AUTHORS:
Cheikh Tidiane Mbaye, Christ Momo Tsague, Florent Tshibwid A. Zeng, Cheikh Diouf
KEYWORDS:
Apple-Peel Configuration, Jejunal Atresia, Intestinal Malrotation
JOURNAL NAME:
Open Journal of Pediatrics,
Vol.15 No.5,
September
8,
2025
ABSTRACT: The combination of jejunal atresia with an apple-peel configuration and intestinal malrotation is extremely rare. This malformative association poses significant surgical and prognostic challenges, particularly in low- and middle-income countries (LMICs), where prenatal diagnosis is rarely established and postoperative resources remain limited. We report the case of a newborn with this association, complicated by extensive small bowel necrosis. Detorsion of the volvulus was performed, followed by resection of the entire necrotic small intestine. This led to short bowel syndrome, the severity of which was exacerbated by the unavailability of parenteral nutrition. The postoperative course was complicated by severe malnutrition and electrolyte disturbances. This report aims to describe a rare case and to highlight the challenges faced in a resource-limited setting.