TITLE:
Heart Disease Scleroderma Revelators: About a Clinical Case
AUTHORS:
Coumba Thiam, Boubacar Sonfo, Youssouf Camara, Asmaou Keita, Mariam Sako, Békaye Traoré, Djeneba Koné, Mamadou Touré, Massama Konaté, Hamidou Oumar Bâ, Ibrahima Sangaré, Sanoussi Daffe, Daouda Fofana, Mariam Cheick Traoré, Boureima Dembélé, Boubacar Diarra, Hamidou Camara, Samba Sidibé, Souleymane Coulibaly, Ichaka Menta, Ousmane Faye
KEYWORDS:
Heart Failure, Scleroderma, Young Subject
JOURNAL NAME:
World Journal of Cardiovascular Diseases,
Vol.13 No.9,
September
25,
2023
ABSTRACT: Scleroderma (or systemic sclerosis) is a disease characterized by
abnormalities in the functioning of small blood vessels and the immune system,
ultimately leading to inflammation and excessive fibrosis of the skin and
various organs, including the heart. Management must be multidisciplinary, to avoid
complications that are often serious. We report the case of a 20-year-old
patient with no known cardiovascular history who consults for dyspnea, and retrosternal pain
associated with a dry cough. On physical examination, she had tachycardia,
swelling of the lower limbs, jugular turgidity, and deafening heart sounds. Cardiac Doppler ultrasound
shows dilation of the right cavities, paradoxical septum and significant
pulmonary arterial hypertension, pericardial effusion of medium abundance. On
oral examination, it presents an ulceration of the lips, dermatological
examination finds scattered hypo chromic spots in the body, more accentuated in
the face. Before the hypo chromic dermatosis, a dermatological consultation was
carried out with an autoimmune assessment that came back positive for systemic
scleroderma.