TITLE:
Osteofibrous Dysplasia-Like Adamantinoma of the Tibia Diagnosed at Age 6 Years Progressing into a Classic Adamantinoma over 39 Years, Reconstruction Performed by a Modified Capanna Technique: A Case Report
AUTHORS:
G. Ulrich Exner, Pascal A. Schai, Tobias C. Bühler, Michael O. Kurrer, Natasha Forster
KEYWORDS:
Osteofibrous Dysplasia-Like Adamantinoma, Tibia, Classic Adamantinoma, Capanna Technique, Pasteurized Autograft
JOURNAL NAME:
Open Journal of Orthopedics,
Vol.12 No.7,
July
26,
2022
ABSTRACT: Background: It is generally accepted that there is a spectrum ranging from
Osteofibrous Dysplasia (OFD) to Osteofibrous dysplasia-like Adamantinoma
(OFD-AD) to “classic” Adamantinoma (AD). However, it is controversial
whether OFD may progress into OFD-AD and AD or these pathologic
changes reflect sampling issues. We herein report the fifth case of late development
of AD from OFD-AD to underline the importance of long-term follow-up. Case: At 6 years bone biopsy of the tibia revealed the diagnosis of
OFD-AD, confirmed by repeat biopsies until the age of 18 years. At age 45
years a progressive focal osteolysis was biopsied and showed histologically a
classic AD. The affected tibial diaphysis was resected and pasteurized. Reconstruction
was performed adapting the “Capanna technique” of inserting the
ipsilateral mobilized fibula into the replanted autologous, pasteurized tibial
segment as biologic stabilizer. At 1.5 years follow-up, the reconstruction has
healed allowing full weight bearing.