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has been cited by the following article:

• TITLE: Heart Disease Scleroderma Revelators: About a Clinical Case

  AUTHORS: Coumba Thiam, Boubacar Sonfo, Youssouf Camara, Asmaou Keita, Mariam Sako, Békaye Traoré, Djeneba Koné, Mamadou Touré, Massama Konaté, Hamidou Oumar Bâ, Ibrahima Sangaré, Sanoussi Daffe, Daouda Fofana, Mariam Cheick Traoré, Boureima Dembélé, Boubacar Diarra, Hamidou Camara, Samba Sidibé, Souleymane Coulibaly, Ichaka Menta, Ousmane Faye

  KEYWORDS: Heart Failure, Scleroderma, Young Subject

  JOURNAL NAME: World Journal of Cardiovascular Diseases, Vol.13 No.9, September 25, 2023

  ABSTRACT: Scleroderma (or systemic sclerosis) is a disease characterized by abnormalities in the functioning of small blood vessels and the immune system, ultimately leading to inflammation and excessive fibrosis of the skin and various organs, including the heart. Management must be multidisciplinary, to avoid complications that are often serious. We report the case of a 20-year-old patient with no known cardiovascular history who consults for dyspnea, and retrosternal pain associated with a dry cough. On physical examination, she had tachycardia, swelling of the lower limbs, jugular turgidity, and deafening heart sounds. Cardiac Doppler ultrasound shows dilation of the right cavities, paradoxical septum and significant pulmonary arterial hypertension, pericardial effusion of medium abundance. On oral examination, it presents an ulceration of the lips, dermatological examination finds scattered hypo chromic spots in the body, more accentuated in the face. Before the hypo chromic dermatosis, a dermatological consultation was carried out with an autoimmune assessment that came back positive for systemic scleroderma.