TITLE:
First Case of Von Willebrand Disease in Niger
AUTHORS:
Amadou Djibrilla-Almoustapha, Moustapha Maman-Brah, Moustapha Elhadji-Chefou, Maman Rabiou Badé, Amal Al-Azhari, Youssoufa Seydou-Moussa, Maman Aminou Mahamane Sani, Mamane Daou, Souleymane Brah, Badé Malam-Abdou
KEYWORDS:
Willebrand Disease, Onco, Hematology, Niamey, Niger
JOURNAL NAME:
Open Journal of Blood Diseases,
Vol.11 No.1,
January
21,
2021
ABSTRACT: Von Willebrand’s disease was first described in 1926 by Erik Von Willebrand. It is a genetic, constitutional defect of hemostasis that is different from hemophilia. It is classified among the rare diseases whose clinical manifestations are dominated by a hemorrhagic profile, which varies from patient to patient. It is an easily diagnosed disease based on a quantitative and qualitative bioassay of VWF. Treatment is multidisciplinary and is based on well-structured prevention. We report the first case of von Willebrand disease in Niger, diagnosed in the Hematology Department of Niamey’s National Hospital.