TITLE:
Right Ventricular Thrombus and Tricuspid Valve Dysfunction in a Patient with Behçet’s Disease
AUTHORS:
Federica Valente, Christian Motet, Stefan Rusu, Frederic Vandergheynst
KEYWORDS:
Behçet’s Disease, Cardiac Involvement, Intracardiac Thrombosis, Tricuspid Valve Regurgitation, Endomyocardial Fibrosis
JOURNAL NAME:
Case Reports in Clinical Medicine,
Vol.9 No.10,
October
21,
2020
ABSTRACT: Background: Behçet’s disease (BD) is a multisystemic, chronic inflammatory disorder with a broad range of manifestations including within the cardiovascular system. Cardiac involvement like intracardiac thrombus (ICT) and valvular involvement in BD are rarely seen entities and often associated with poor prognosis. Case Presentation: We present the case of a young patient with vascular-Behçet diagnosed by the presence of intracardiac thrombus in the right ventricle, unresponsive to medical treatment. Even though the intracardiac lesion was successfully treated by surgical excision, he presented a severe tricuspid dysfunction some years later due to the extension of fibrosis with no surgical therapeutic option. Conclusion: Intracardiac thrombosis is a rare but early manifestation of Behçet’s disease, which is difficult to diagnose and has a poor prognosis.