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Hypocalcified autosomal recessive amelogenesis imperfecta—A case report

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DOI: 10.4236/ojst.2012.24044    4,847 Downloads   7,026 Views   Citations


Amelogenesis imperfecta is an unusual hereditory disorder affecting both primary and permanent dentition. We present a rare case of hypocalcified auto-somal recessive amelogenesis imperfecta occuring in primary dentition in a 7-year-old girl with a family history of consanguineous marriage. Clinical and radiological examination revealed discoloration and hypoplasia of enamel with easy chipping affecting both maxillary and mandibular dentition.

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The authors declare no conflicts of interest.

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Dawasaz, A. , Zakirulla, M. and Allahbaksh, M. (2012) Hypocalcified autosomal recessive amelogenesis imperfecta—A case report. Open Journal of Stomatology, 2, 251-254. doi: 10.4236/ojst.2012.24044.


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