A rare clinical presentation of pulmonary hypoplasia

Figen Gülen, Sakine Kar, Levent Midyat, Esen Demir, Süphan Özyurt, Arif Ruhi Özyürek, Remziye Tanaç, Naim Ceylan

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DOI: 10.4236/ojped.2011.14018                

Abstract

Pulmonary hypoplasia is a rare congenital anomaly, which is frequently associated with other congenital anomalies. Clinical symptoms vary depending on the other system anomalies and severity of pulmonary hypoplasia. Although it is usually diagnosed in infancy and childhood, some cases do not show any symptoms until the adolescent ages. In adolescents and adults with unilateral hypolucent lung, although it is seen rarely, pulmonary hypoplasia should always be kept in mind. In this article, we present a case with pulmonary hypoplasia who remained asymptomatic until puberty.

Keywords

Lung; Unilateral; Hypoplasia; Adolescent

Conflicts of Interest

The authors declare no conflicts of interest.

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