Open Journal of Rheumatology and Autoimmune Diseases

Volume 11, Issue 2 (May 2021)

ISSN Print: 2163-9914   ISSN Online: 2164-005X

Google-based Impact Factor: 0.26  Citations  

AA Amyloidosis Secondary to Primary Sjögren Syndrome: Can It Be Developed without Chronic Inflammation?

HTML  XML Download Download as PDF (Size: 630KB)  PP. 29-35  
DOI: 10.4236/ojra.2021.112004    545 Downloads   1,927 Views  Citations

ABSTRACT

Background: The association of primary Sjögren syndrome (PSS) and AA amyloidosis is a rare occurrence. Objective: To describe the phenotype of patients with this association through our two cases and a literature review. Materials and methods: A report of two cases of AA amyloidosis complicating primary Sjögren syndrome with a literature review. Results: Eight patients of Primary Sjögren’s Syndrome complicated by AA amyloidosis were studies. Six cases were reported in the literature by consulting several databases. 50% of patients had a positive immunological assessment, three cases with kidney damage, and three cases lung damage. Conclusion: The immunological activity in the Primary Sjogren’s Syndrome requires the search not only a lymphoma but also AA amyloidosis apart from any clinical or biological chronic inflammation.

Share and Cite:

Zaher, S. , Nassar, K. , Razzouki, I. , Regragui, M. , Karkouri, M. and Janani, S. (2021) AA Amyloidosis Secondary to Primary Sjögren Syndrome: Can It Be Developed without Chronic Inflammation?. Open Journal of Rheumatology and Autoimmune Diseases, 11, 29-35. doi: 10.4236/ojra.2021.112004.
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