Author(s)

Thierry Mukenge Wa Mukengeshay^1*, Fatoumata Binta Balde¹, Zineb Benmassaoud¹, Priscilla Kinsala², Othmane Allaoui^1,3, Abdelhalim Mahmoudi^1,3, Khalid Khattala^1,3, Sara Benmilloud², Youssef Bouabdallah^1,3

¹Service de Chirurgie Pédiatrique, Centre Hospitalier et Universitaire Hassan II de Fès, Fès, Morocco.
²Service de Pédiatrie, Unité d’Oncologie, Centre Hospitalier et Universitaire Hassan II de Fès, Fès, Morocco.
³Faculté de Médecine et de Pharmacie, Université Sidi Mohamed Ben Abdallah de Fès, Fès, Morocco.

Introduction: This study aims to describe the outcome of adrenocortical cancer in children through observation. Observation: A 10-year-old girl with no previous pathological history. She presented headaches and severe hypertension with clinical and biological signs of hyperandrogenism for 6 months. An abdominal CT scan showed an encapsulated left adrenal mass without local or regional invasion or secondary location. A pheochromocytoma or adrenal neuroblastoma was first suspected. The blood pressure was stable at 130/65 mmHg under antihypertensive drugs. She underwent a complete tumor resection without any intraoperative incident. The pathologic study confirmed the adrenocortical carcinoma scored Weiss 7. The severe high blood pressure reappeared 2-year later despite antihypertensive drugs. The thoracic abdominal and pelvic CT scan showed a locally advanced tumor recurrence in the left adrenal gland with parenchymal nodes in the lungs and liver. The outcome was fatal despite medical and surgical management. Conclusion: Adrenocortical cancer is a rare tumor. It is important to hormonal testing in the presence of Cushing’s syndrome in children. It can give a strong indication of the diagnostic possibilities. Histology confirms the diagnosis. The evolution is covered by complications, in particular recurrence with life-threatening metastases.

Adrenal Tumor, Adrenal Cortex, Hyperandrogenism, Child

Mukengeshay, T. , Balde, F. , Benmassaoud, Z. , Kinsala, P. , Allaoui, O. , Mahmoudi, A. , Khattala, K. , Benmilloud, S. and Bouabdallah, Y. (2022) Corticosurrenaloma: About a Pediatric Case. Open Journal of Pediatrics, 12, 449-452. doi: 10.4236/ojped.2022.122048.