Idiopathic Intracranial Hypertension in Sickle Cell Disease: A Paediatric Case Report

Bharath Gowda, Sanjay Sahi

Department of Paediatrics, Queen Mary’s Hospital, Sidcup, UK.

DOI: 10.4236/nm.2013.44033                

Abstract

In this article, we present the case of a 12-year-old girl with sickle cell disease (SCD), who presented with the severe headache. She had bilateral 6th cranial nerve palsy and papilloedema. The common sickle cell-related vascular causes of headache were ruled out by neuro-imaging. She then had a lumbar puncture and was diagnosed with idiopathic intracranial hypertension (IIH). This case demonstrates that IIH can affect younger children with SCD and should form a part of differential diagnosis when investigating causes of headache in SCD.

Keywords

Sickle Cell Disease; Idiopathic Intracranial Hypertension; Headache in Children

Conflicts of Interest

The authors declare no conflicts of interest.

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