Solid-Pseudopapillary tumor of the pancreas: Clinical and radiological features. Case report and review of the literature

Slim Jarboui, Alifa Daghfous, Karima Kacem, Lamia Rezgui Marhoul

Department of General Surgery, Sidi Bouzid Hospital, Sidi Bouzid, Tunisia.
Department of Hematology, Aziza Othmana Hospital, Tunis, Tunisia.
Department of Radiology, Trauma Center of Ben Arous, Ben Arous, Tunisia.

DOI: 10.4236/crcm.2013.27110                

Abstract

Solid-Pseudopapillary Tumor (SPT) of the pancreas is considered to be a rare pancreatic tumor that occurs in young females. Most SPTs are considered to be benign. However, the natural course of history has not yet been clarified. We reported a case of 25-year-old women with a patent history of splenectomy for hemolytic anemia, who presented intermittent abdominal pain and vomiting of 6 months ago. Physical examination revealed a hard mass of 8 × 5 cm in the left upper quadrant of the abdomen. Routine laboratory tests were within the normal range. CT-Scan showed an 8 × 6 cm lesion with irregular low density in the body and the tail of the pancreas. MRI showed a mass of 8 cm, surrounded by a capsule, with the irregular intensity both in T1 and T2 enhanced-images. Distal pancreatictomy was done as a definitive treatment via a Bi sub costal incision. Histopathological examination confirmed the diagnosis of SPT. There was no vascular invasion or other malignant features. The resection margins are free of lesions. The post operative course was uneventful. During post operative follow-up of 24 months, there is no sign of recurrence on CT-scan. SPT is a rare condition with a low potential for malignancy and favorable prognosis. Surgical resection is generally curative. Characteristic CT and MRI scans combined with age and sex profile should be sufficient for the diagnosis and the decision to operate.

Keywords

Soli-Pseudopapillary Tumor; Distal Pancreatectomy; Pancreas

Conflicts of Interest

The authors declare no conflicts of interest.

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