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Nevoid basal cell carcinoma: Case report

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DOI: 10.4236/ojst.2014.41006    2,971 Downloads   3,960 Views   Citations

ABSTRACT

Nevoid basal cell carcinoma, known as Gorlin Goltz Syndrome, is a rare hereditary condition, characterized by a wide range of developmental abnormalities and a predisposition to neoplasms. In this report, we discuss a case of a patient with Gorlin Goltz Syndrome, who was 16 years old when first admitted for an initial appointment. The patient was diagnosed, treated and followed up for 7 years to present day. This syndrome is associated with a broad spectrum of anomalies and neoplasms as basal cell carcinomas, odontogenic keratocysts, palmar and/or plantar pits, and ectopic calcifications of the falx cerebri. It affects multiple organ systems, which include skeletal, teeth, jaw, skin, eyes, reproductive organs, and neural system. All the features however, are rarely observed in a single patient. The following paper presents the significance of early diagnosis of Gorlin Goltz Syndrome and the importance of a multidisciplinary approach in providing proper treatment for the patient.

Conflicts of Interest

The authors declare no conflicts of interest.

Cite this paper

Agani, Z. , Loxha, M. , Krasniqi, V. , Ahmedi, J. , Namani, A. and Murtezani, A. (2014) Nevoid basal cell carcinoma: Case report. Open Journal of Stomatology, 4, 29-32. doi: 10.4236/ojst.2014.41006.

References

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