Author(s)

Jimmy Zúñiga-Márquez^1*, Nataly Gutierrez-Ávila¹, Patricia Quintero-Cusgüen¹, José Traslaviña-Sierra², Leidy Salazar-Tapiero², Lady Carrillo-Alba², Lina Caquimbo-Salazar², Claudia Murillo-Espinosa², Michel Hernández¹

¹Hospital Universitario de la Samaritana, Bogotá, Colombia.
²Neuropsychological Assessment and Diagnosis Specialization Program, School of Psychology, Universidad San Buenaventura Bogotá, Bogotá, Colombia.

Susac Syndrome (SS) is an autoimmune disease characterized by the clinical triad of encephalopathy, hearing loss and retinal arterial occlusions, with prevalent structural changes identified on brain magnetic resonance imaging (white matter, corpus callosum, basal ganglia region and the thalamic region extending to the midbrain) in the majority of cases, which lead to cognitive manifestations of which there is a paucity of descriptions in the literature. The objective of this case study is to compare to post-rehabilitation neurocognitive profile of a 29-year-old woman with SS presenting with compromised intellectual and motor skills and cognitive functions, together with neuropsychiatric symptoms. Better performance was found in the neuropsychological assessment, with changes in the structural cerebral network evidenced on Diffusion Tensor Imaging (DTI) performed following the therapeutic and pharmacological intervention.

Susac Syndrome, Demyelinating Disease, Neuropsychological Assessment, Rehabilitation

Zúñiga-Márquez, J. , Gutierrez-Ávila, N. , Quintero-Cusgüen, P. , Traslaviña-Sierra, J. , Salazar-Tapiero, L. , Carrillo-Alba, L. , Caquimbo-Salazar, L. , Murillo-Espinosa, C. and Hernández, M. (2021) Comparative Analysis of Post-Rehabilitation Neuropsychological Profile of a Patient with Susac Syndrome—A Case Report. Neuroscience and Medicine, 12, 79-89. doi: 10.4236/nm.2021.123007.