TITLE:
Erdheim-Chester Disease with Right Atrial Tumor and “Temporal Arteritis”
AUTHORS:
Joseph Skalski, William D. Edwards, Eric L. Matteson
KEYWORDS:
Erdheim-Chester Disease; Temporal Arteritis; Giant Cell Arteritis
JOURNAL NAME:
Open Journal of Rheumatology and Autoimmune Diseases,
Vol.2 No.3,
August
21,
2012
ABSTRACT: Erdheim-Chester disease is an unusual syndrome characterized by non-Langerhans cell histiocytosis which can mimic rheumatologic diseases. We report a case of Erdheim-Chester masquerading as giant cell arteritis, which was success-fully managed with anakinra as anti IL-1 therapy.