TITLE:
First Case of Liver Glycogen Documented in the Pediatric Ward of the University Hospital of Treichville (Cote D’Ivoire)
AUTHORS:
Jean-Jacques Yao Atteby, Lassina Cissé, Jacob Enoh, Kouadio Richard Azagoh, Germaine Niamké, Daouda Koné, Joseph Ouattara, Evelyne Kouadio, Beugre Martine Niangué, Soumahoro Mathurin Oulai, Joseph Andoh
KEYWORDS:
Hepatic, Glycogenosis, Metabolic Disease, Child
JOURNAL NAME:
Open Journal of Pediatrics,
Vol.7 No.2,
June
13,
2017
ABSTRACT: The authors report a case of hepatic glycogen storage diseases type III (Cori-Forbes disease) of a Métis 3-year-old girl born and resident in C?te d'Ivoire. The discovery of this disease was made at the age of 2 years in the diagnosis of abdominal mass in a child subject to frequent hypoglycemia. The management currently consists of a diet enriched with glucose and maltose dextrin. We note in our case, a failure to thrive despite the persistent support.