TITLE:
Case Report of Prosthetic Treatment of a Young Patient Suffering Papilon-Lefever Syndrome
AUTHORS:
Masoumeh Rostamzadeh, Ghasem Omati Shabestari, Mohammad Rastegar Khosravi
KEYWORDS:
Prosthetic Treatment, Young Patient, Papilon-Lefever Syndrome
JOURNAL NAME:
International Journal of Clinical Medicine,
Vol.8 No.6,
June
28,
2017
ABSTRACT: Papillon-Lefevre syndrome (PLS) is a rare recessive autosomal disease which occurs with palms and soles hyperkeratosis as well as primary and permanent teeth periodontal loss. Recently, it has been proved that a mutation at Cathepsin gene C is the genetic cause of PLS. All primary and permanent teeth of the patients are lost at ages 2 or 3 because of serious alveolar bone destruction. This paper presents a complete case of prosthetic treatment of an 8-year old girl with PLS.