Vein of Galen Malformations: Case Report & Review

Snigdha Goyal^1*, Sunder Goyal², Isha Saini², Sarita Bishnoi³

¹Department of Pathology, Dr. RML Postgraduate Institute of Medical Sciences & Research, New Delhi, India.
²Department of Surgery, Kalpana Chawla Government Medical College, Karnal, India.
³Department of Radiology, Kalpana Chawla Government Medical College, Karnal, India.

DOI: 10.4236/oalib.1101478                

Abstract

Vein of Galen aneurysmal malformations (VGAMs) are rare congenital abnormalities that can cause severe morbidity and mortality. VGAMs present in different way from vein of Galen aneurysmal dilatations (VGADs). The VGAMS have a parenchymal arteriovenous malformation that drains through the vein of Galen whereas VGADs may present with intracranial hemorrhage. In neonates VGAMs result in high-output cardiac failure. Surgery offers little improvement, with fatal outcomes in 80% to 100% of cases.

Keywords

Vein of Galen Aneurysmal Malformation, Vein of Galen Aneurysmal Dilatation

Conflicts of Interest

The authors declare no conflicts of interest.

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