Adult Langerhans Cell Histiocytosis: A Rare Etiology of Spinal Cord Compression

Fadila Kouhen^1*, Naoual Benhmiddou¹, Mohammed Afif¹, Fadoua Rais¹, Youssef Mahdi², Basma Khannoussi², Khadija Bellahamou³, Ibrahim Ghissassi³, Khouloud Boussouni⁴, Hanan Elkacemi¹, Sanaa Elmajjaoui¹, Tayeb Kebdani¹, Noureddine Benjaafar¹

¹Department of Radiotherapy, National Institute of Oncology, Rabat, Morocco.
²Department of Pathology, National Institute of Oncology, Rabat, Morocco.
³Department of Medical Oncology, National Institute of Oncology, Rabat, Morocco.
⁴Department of Radiology, National Institute of Oncology, Rabat, Morocco.

DOI: 10.4236/ojim.2015.53005                

Abstract

Langerhans cell histiocytosis is a rare disease involving clonal proliferation of langerhans cells seen in children and young adults. Clinical presentation is variable, ranging from a single location in the bone to severe multivisceral involvement. Moreover, spinal involvement causing myelopathy is even rare and unusual. We report a rare case of adult Langerhans cell histiocytosis in the dorsal spine causing a spinal cord compression associated with a pulmonary process treated by surgery, radiotherapy and systemic therapy with good evolution.

Keywords

Langerhans Cell Histiocytosis, Adults, Spinal Cord Compression

Conflicts of Interest

The authors declare no conflicts of interest.

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