Lymphoepithelioma-Like Carcinoma of Parapharyngeal Space—A Case Report with Review of Literature

Produl Hazarika^1*, Seema Elina Punnoose¹, John Victor¹,   Sreekala², Nirmali Dutta³

¹Department of ENT, NMC Specialty Hospital, Abu Dhabi, UAE.
²Department of Pathology, NMC Specialty Hospital, Abu Dhabi, UAE.
³Department of Radiology, NMC Specialty Hospital, Abu Dhabi, UAE.

DOI: 10.4236/ijohns.2015.42028                

Abstract

Extra-nasopharyngeal lymphoepithelioma-like carcinomas (LELC) are uncommon epithelial tumors. A few isolated case reports and series are available in literature involving the larynx, pharynx, salivary gland, lung etc., but involvement in the parapharyngeal space has not yet been reported. We aim to highlight one such case that has a clinical and radiological characteristic of a benign lesion whilst the histopathology reveals an infiltrating neoplasm. The typical clinical aggressiveness of a classical LELC of extra-nasopharyngeal lesion as described in literature is not present in our case. Also seen is an uncommon finding of abnormal branching of left external carotid artery. There is no standard treatment protocol for such a tumor; however, wide excision of this tumor in the parapharyngeal space via trans-cervical, trans-mandibular, trans-palatal approach has shown good and satisfactory tumor control of the primary site so far.

Keywords

Lymphoepithelioma-Like Carcinoma (LELC), Parapharyngeal Space, Trans-Cervical, Trans-Mandibular, Cells in Cords, Lymphoplasmacytoid

Conflicts of Interest

The authors declare no conflicts of interest.

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