Pneumonectomy in a Patient with Swyer-James-MacLeod Syndrome

Mariana Vigiola Cruz¹, Gregory D. Trachiotis^1,2*

¹The Division of Cardiothoracic Surgery, Veterans Affairs Medical Center, Portland, USA.
²The George Washington University, Washington DC, USA.

DOI: 10.4236/ss.2015.62009                

Abstract

Swyer-James-MacLeod syndrome is a rare disease that results in parenchymal damage believed to be caused by recurrent lung infections in childhood. We report a case of a previously healthy young woman that presented with insidious progression of exertional dyspnea with restrictive lung physiology. Axial imaging demonstrated a hyperinflated emphysematous right lung with lower lobe fibrosis, nodules and air-fluid filled cysts, with a small right pulmonary artery and contralateral shifting of the mediastinum. She underwent right pneumonectomy ultimately resulting in improvement of her symptoms, with surgical pathology indicating extensive emphysema, bronchiec- tasis, fibrosis with osseous metaplasia, and placental transmogrification of alveolar septa, being consistent with a diagnosis of SJMS.

Keywords

Swyer-James, Hyperlucent Lung, Pneumonectomy

Conflicts of Interest

The authors declare no conflicts of interest.

References

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