Ectopic Autosomal Dominant Polycystic Kidney Disease (ADPKD)—An Extremely Rare Radiological Finding

Manish Gupta

Department of Medicine, Gajra Raja Medical College, Gwalior, India.

DOI: 10.4236/ojrad.2014.41015                

Abstract

ADPKD is an inherited systemic disorder that predominantly affects the kidney, but may affect other organs including liver, pancreas, brain, and arterial blood vessel. APKPD occurs worldwide affecting about 1 in 500 - 1000 people. Hypertension is the most common manifestation of ADPKD and the major contributor to renal disease progression. A definite diagnosis of ADPKD relies on image testing. Renal ultrasound is commonly used because of its cost effectiveness.

Keywords

Ectopic; Pelvic Kidney; ADPKD; Polycystic; Radiological Diagnosis

Conflicts of Interest

The authors declare no conflicts of interest.

References

[1]	Chen, D.P., Ma, Y.Y., Mao, Z.G. and Mei, C.L. (2010) Ectopic (Pelvic) Autosomal Dominant Polycystic Kidney Disease. Internal Medicine, 49, 2525-2526. http://dx.doi.org/10.2169/internalmedicine.49.4415
[2]	Solak, Y., Biyik, Z., Gaipov, A., Ozbek, O. and Tonbul, H.Z. (2012) Ectopic, Polycystic and Stoned: Pelvic Kidney in a Patient with Autosomal Dominant Polycystic Kidney Disease. The American Journal of the Medical Sciences, 343, 418. http://dx.doi.org/10.1097/MAJ.0b013e3182373e89
[3]	Connori, A., Weston, C.E., Dick, C. and Taylori, J.E. (2009) Autosomal Dominant Polycystic Kidney Disease Complicating Renal Ectopia and Managed with Renal Transplantation. NDT Plus, 2, 420. http://dx.doi.org/10.1093/ndtplus/sfp075
[4]	Malek, R.S., Kelalis, P.P. and Burke, E.C. (1971) Ectopic Kidney Tissue in Children and Frequency of Association with Other Malformation. Mayo Clinic Proceedings, 46, 461.
[5]	Sheih, C.P., Liu, M.B., Hung, C.S., et al. (1989) Renal Abnormalities in School Children. Pediatrics, 84, 1086.
[6]	(2012) Autosomal Dominant Kidney Disease with Contralateral Agenesis. Nefrologia, 32, 839-842.
[7]	Torres, V.E., Harris, P.C. and Pirson, Y. (2007) Autosomal Dominant Polycystic Kidney Disease. Lancer, 369, 12871301. http://dx.doi.org/10.1016/S0140-6736(07)60601-1