Cor-triatriatum dexter with pulmonary hypertension in a neonate

Bijay Kumar Meher, Pradeep S, Leena Das, Priyadarsi Tripathy

Department of Cardiology, SCB Medical College, Cuttack, India.
PG Department of Paediatrics SVPPGIP, SCB Medical College, Cuttack, India.

DOI: 10.4236/ojped.2013.34060                

Abstract

Cor-triatriatum dexter is an extremely rare congenital anomaly, in which right atrium is divided into 2 halves by a septum giving rise to 3 atrial chambers. We report here a case of cor-triatriatum dexter who presented at 3 days of life with tachypnea and did not respond to antibiotics. Echocardiography revealed ostium secundum atrial septal defect (ASD) with right to left flow, intact interventricular septum (IVS), severe tricuspid regurgitation with pulmonary arterial hypertension and a membranous structure dividing right atrium into 2 halves with good biventricular function. The patient improved with sildenafil and anti-failure medication. This case of cor-triatriatum dexter presenting with pulmonary hypertension, tricuspid regurgitation and ASD added to the new spectrum of cor-triatriatum dexter.

Keywords

Cor-Triatriatum; Pulmonary Hypertension; Neonate

Conflicts of Interest

The authors declare no conflicts of interest.

References

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