Epitheloid Leiomyosarcoma of the Jejunum Presenting with Intussusception in a Young Adult Male: A Case Report

John O. Obafunwa, Christopher Pritchett, Siva Maikandanathan, Dahiru Adamu Garkuwa

Department of Pathology and Forensic Medicine, Lagos State University Teaching Hospital, Lagos, Nigeria.
Department of Surgery, South Tyneside District Hospital, South Shields, UK.

DOI: 10.4236/ss.2013.45055                

Abstract

A 27-year-old male presented with intestinal obstruction due to a jejuno-jejunal intussusception, 23 years after a childhood nasopharyngeal carcinoma. He was successfully treated for the latter by radiotherapy but subsequently required a mandibuloplasty for presumably facial hypoplasia sequel to the radiotherapy. The present intussusception was resected with wide margins revealing a partly haemorrhagic, polypoid and sessile jejunal tumour measuring 7.7 × 3.5 × 2.6 cm. Microscopy with extensive immunohistochemical studies revealed a relatively rare and highly malignant epitheloid leiomyosarcoma arising from the muscularis propria with extension to the mucosa and serosa. No metastases were found and post-operative follow-up has so far been uneventful. The present case of a malignant tumour presenting as an intussusception in a young adult, was unrelated to a childhood malignant tumour in the same patient. The former was successfully treated by a wide excision in support of the advocated surgical approach to adult intussusception.

Keywords

Epitheloid Leiomyosarcoma; Intussusception; Surgical Resection

Conflicts of Interest

The authors declare no conflicts of interest.

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