Malignant Triton Tumor in the Abdominal Wall: A Case Report

Yoshiyuki Kitamura, Koichiro Abe, Shingo Baba, Takuro Isoda, Yasuhiro Maruoka, Yoshio Matsuo, Yuichiro Kubo, Akio Sakamoto, Hiroshi Nishimura, Masayuki Sasaki, Hiroshi Honda

Department of Anatomic Pathology, Pathological Sciences, Graduate School of Medical Sciences, Kyushu University, Fukuoka, Japan.
Department of Clinical Radiology, Kyushu University Hospital, Fukuoka, Japan.
Department of Clinical Radiology, Saiseikai Futsukaichi Hospital, Fukuoka, Japan.
Department of Health Sciences, Graduate School of Medical Sciences, Kyushu University, Fukuoka, Japan.
Department of Orthopaedic Surgery, Kyushu University Hospital, Fukuoka, Japan.

DOI: 10.4236/ami.2013.32002                

Abstract

Malignant triton tumor (MTT) is a rare variant of malignant peripheral nerve sheath tumor (MPNST) with rhabdomyosarcomatous differentiation. We report the case of a 54-year-old male without a history of neurofibromatosis type 1 (NF1) who had a growing abdominal wall tumor diagnosed as MTT. Computed tomography (CT), magnetic resonance imaging (MRI) and 2-[F-18]-fluoro-2-deoxy-D-glucose positron emission tomography/CT (FDG-PET/CT) were performed. The MRI and FDG-PET/CT indicated that the lateral component of the tumor was composed of many proliferative cells, corresponding to the histopathological finding of a cellular proliferation of spindle-shaped cells. In light of this case and previous reports, it is apparent that FDG-PET/CT is a helpful tool for distinguishing MTT from benign peripheral nerve sheath tumor.

Keywords

Malignant Triton Tumor (MTT); Malignant Peripheral Nerve Sheath Tumor (MPNST); 2-[F-18]-Fluoro-2-Deoxy-D-Glucose Positron Emission Tomography/Computed Tomography (FDG-PET/CT)

Conflicts of Interest

The authors declare no conflicts of interest.

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