Erdheim-Chester Disease with Right Atrial Tumor and “Temporal Arteritis”

Joseph Skalski, William D. Edwards, Eric L. Matteson

Department of Internal Medicine, Mayo Clinic College of Medicine, Rochester Minnesota, USA.
Department of Pathology, Mayo Clinic College of Medicine, Rochester, USA.
Division of Rheumatology, Mayo Clinic College of Medicine, Rochester, USA.

DOI: 10.4236/ojra.2012.23008                

Abstract

Erdheim-Chester disease is an unusual syndrome characterized by non-Langerhans cell histiocytosis which can mimic rheumatologic diseases. We report a case of Erdheim-Chester masquerading as giant cell arteritis, which was success-fully managed with anakinra as anti IL-1 therapy.

Keywords

Erdheim-Chester Disease; Temporal Arteritis; Giant Cell Arteritis

Conflicts of Interest

The authors declare no conflicts of interest.

References

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