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Chordomas and Their Consideration in the Radiographic Differential of Extra-Axial Lesions of the Central Nervous

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DOI: 10.4236/ojmn.2012.23012    3,809 Downloads   6,843 Views   Citations


Due to the rare occurrence of chordomas extra-axially, these lesions have not earned a great deal of consideration in the clinical and radiographic differential diagnoses of extra-axial paraspinal lesions. We describe a case of a patient with a surgically resected extra-axial chordoma and review the radiologic characteristics of chordomas as an entity in the spectrum of extra-axial lesions. A 47-year-old man presented to our institution with four months of intermittent parethesias, pain, and subjective weakness in the left leg. MR imaging of the lumbar spine demonstrated a large heterogeneously- enhancing paraspinal lesion extending from the left L3-4 neural foramen into the psoas muscle. The patient underwent a CT-guided needle biopsy demonstrating features consistent with a chordoma. He then underwent a left retroperitoneal approach and en bloc resection of the lesion from the vertebral column. Pathology confirmed chordoma as the diagnosis. EACs are a rare but important consideration in the diagnosis of extra-axial lesions of the central nervous system.

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S. Lang, J. Thawani, A. Sayah, S. Venneti, D. Brewington, E. Zager and S. Dante, "Chordomas and Their Consideration in the Radiographic Differential of Extra-Axial Lesions of the Central Nervous," Open Journal of Modern Neurosurgery, Vol. 2 No. 3, 2012, pp. 58-62. doi: 10.4236/ojmn.2012.23012.

Conflicts of Interest

The authors declare no conflicts of interest.


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