A Rare Cause of Melaena-Duodenal Gangliocytic Paraganglioma


Gangliocytic paraganglioma (GP), a rare tumour that arises most frequently from the periampullary area, is considered to be a benign neoplasm with a potential for lymphatic spread. Distant metastases are rare [1]. We report a case of a 51 year old female who presented with abdominal pain, anaemia and melaena. Endoscopy, push enteroscopy and biopsy revealed a periampullary neuroendocrine tumour. Immunohistochemistry of the pancreatic duodenectomy specimen demonstrated a duodenal gangliocytic paraganglioma with no lymph node metastases. We review the literature on this rare tumour and the current treatment protocol.

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C. Esquivel, S. Navadgi, G. Otto and R. Thomas, "A Rare Cause of Melaena-Duodenal Gangliocytic Paraganglioma," Surgical Science, Vol. 3 No. 4, 2012, pp. 232-235. doi: 10.4236/ss.2012.34045.

Conflicts of Interest

The authors declare no conflicts of interest.


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