Author(s)

Amit Lehavi, Hanna Mandel, Yeshayahu (Shai) Katz

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Department of Anesthesiology.

Congenital disorders of glycosylation (CDGs) are group group of genetic defects in the assembly and processing pathway of protein glycosylation, which cause a wide range of multi system dysfunction. This paper describes the anesthetic management of 6 year old boy with CDG type I-x for upper airway surgery. We used a sevoflurane-nitrous oxide-remifentanil regime with no complications and good results. As for now, the literature lacks reports of anesthetic management of children with CDG I-x, and this report may provide clinicians an option for safe anesthetic management.

Anesthesia, Pediatric, Metabolic Disorders, Congenital Disorders of Glycosylation, CDG

A. Lehavi, H. Mandel and Y. Katz, "Anesthetic Management of a Boy with Congenital Disorder of Glycosylation (CDG) I-x," International Journal of Clinical Medicine, Vol. 2 No. 3, 2011, pp. 325-327. doi: 10.4236/ijcm.2011.23056.