Spinal Cord Compression, a Rare Neurofibromatosis Complication - World Journal of Neuroscience

WJNS > Vol.9 No.3, August 2019

World Journal of Neuroscience

Volume 9, Issue 3 (August 2019)

ISSN Print: 2162-2000 ISSN Online: 2162-2019

Google-based Impact Factor: 0.23 Citations h5-index & Ranking

Spinal Cord Compression, a Rare Neurofibromatosis Complication ()

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Download as PDF (Size: 584KB) PP. 191-198

DOI: 10.4236/wjns.2019.93012 742 Downloads 1,947 Views

Author(s)

Habib Abdoul Karim Ouiminga^1*, Sylvain D. Zabsonré², Aminath Kélani³, Souleymane Ouattara⁴, Assane Dravé⁵, Raphael Marie Kabore⁶, Désiré Harouna Sankara⁷, Magatte Gaye⁸

Affiliation(s)

¹Department of Neurosurgery, CHU Tengandogo, Ouagadougou, Burkina Faso.
²Department of Neurosurgery, CHU Yalgado Ouédraogo, Ouagadougou, Burkina Faso.
³Department of Neurosurgery, Hopital National de Niamey, Niger.
⁴Department of Pathology, CHU Tengandogo, Ouagadougou, Burkina Faso.
⁵Department of Neurology, CHU Ouahigouya, Ouahigouya, Burkina Faso.
⁶Department of Neurology, CHU Tengandogo, Ouagadougou, Burkina Faso.
⁷Department of Imagery, CHU Tengandogo, Ouagadougou, Burkina Faso.
⁸Department of Neurosurgery, Hôpital Général Grand Yoff, Dakar, Senegal.

ABSTRACT

Objective: The objective of this study is to report a case of spinal cord compression, which is a rare complication of neurofibromatosis type 1. Observation: We report the case of a 45-year-old man, which presented a syndrome of thoracic spinal cord compression at the stage of spastic paraparesis. Its installation was gradually over 6 months associated with the inaugural back pain. He had a clinical history of neurofibromatosis type 1 with “Café-au-lait” spots. There were multiple painless nodules under the skin of different size on the chest, forearms and legs. A large isolated nodule, purplish was observed on the chest. The neuro-imaging showed a para-spinal anterior mass expansion inside the spinal canal causing spinal compression at the level of the second and third thoracic vertebra. It extends into the intervertebral foramen of the third and fourth thoracic vertebra leading to a scalloping. A second large heterogeneous left intra-abdominal mass containing cyst areas and calcifications was discovered in imaging. After a spinal decompression with laminectomy of the second and third thoracic vertebra, the reduction of pain and motor recovery was gradual. The large nodule excision was performed. Histology found a plexiform neurofibroma. Excision of the left intra-abdominal mass could not be performed because the patient’s consent had not been obtained. Conclusion: The spinal cord compression is a rare complication of neurofibromatosis type 1. However, it is essential to think about it in front of any spinal cord symptoms or any atypical long term spinal pain.

KEYWORDS

Neurofibromatosis, Von Recklinghausen’s Disease, Spinal Cord Compression

Share and Cite:

Ouiminga, H. , Zabsonré, S. , Kélani, A. , Ouattara, S. , Dravé, A. , Kabore, R. , Sankara, D. and Gaye, M. (2019) Spinal Cord Compression, a Rare Neurofibromatosis Complication. World Journal of Neuroscience, 9, 191-198. doi: 10.4236/wjns.2019.93012.

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