Idiopathic Intracranial Hypertension in Sickle Cell Disease: A Paediatric Case Report


In this article, we present the case of a 12-year-old girl with sickle cell disease (SCD), who presented with the severe headache. She had bilateral 6th cranial nerve palsy and papilloedema. The common sickle cell-related vascular causes of headache were ruled out by neuro-imaging. She then had a lumbar puncture and was diagnosed with idiopathic intracranial hypertension (IIH). This case demonstrates that IIH can affect younger children with SCD and should form a part of differential diagnosis when investigating causes of headache in SCD.

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B. Gowda and S. Sahi, "Idiopathic Intracranial Hypertension in Sickle Cell Disease: A Paediatric Case Report," Neuroscience and Medicine, Vol. 4 No. 4, 2013, pp. 215-216. doi: 10.4236/nm.2013.44033.

Conflicts of Interest

The authors declare no conflicts of interest.


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