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Adult Langerhans Cell Histiocytosis: A Rare Etiology of Spinal Cord Compression

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DOI: 10.4236/ojim.2015.53005    3,086 Downloads   3,470 Views   Citations

ABSTRACT

Langerhans cell histiocytosis is a rare disease involving clonal proliferation of langerhans cells seen in children and young adults. Clinical presentation is variable, ranging from a single location in the bone to severe multivisceral involvement. Moreover, spinal involvement causing myelopathy is even rare and unusual. We report a rare case of adult Langerhans cell histiocytosis in the dorsal spine causing a spinal cord compression associated with a pulmonary process treated by surgery, radiotherapy and systemic therapy with good evolution.

Conflicts of Interest

The authors declare no conflicts of interest.

Cite this paper

Kouhen, F. , Benhmiddou, N. , Afif, M. , Rais, F. , Mahdi, Y. , Khannoussi, B. , Bellahamou, K. , Ghissassi, I. , Boussouni, K. , Elkacemi, H. , Elmajjaoui, S. , Kebdani, T. and Benjaafar, N. (2015) Adult Langerhans Cell Histiocytosis: A Rare Etiology of Spinal Cord Compression. Open Journal of Internal Medicine, 5, 21-28. doi: 10.4236/ojim.2015.53005.

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