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A Primary Epithelioid Hemangioendothelioma of the Right Atrium: Report of a Case and Literature Review

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DOI: 10.4236/ojts.2013.32013    3,160 Downloads   4,826 Views   Citations

ABSTRACT

Primary cardiac epithelioid hemangioendothelioma (EHE) is extremely uncommon. To our knowledge, only fourteen cases have been reported. We report a case of a primary EHE of the right atrium which incidentally detected in 77-year-old woman. Echocardiograhpy revealed a 26 × 16 mm right atrial mass attached to the base of the interatrial septum and moderate regurgitation of the tricuspid valve. The tumor and stalk were completely resected from the interatrial septum with a partial resection of the septal leaflet of the tricuspid valve. The patient had an uneventful postoperative course and no signs of recurrence nor metastasis of EHE 4 years after operation. Because of malignant potential of EHE, a longer period of close follow up is necessary.

Conflicts of Interest

The authors declare no conflicts of interest.

Cite this paper

T. Sugimoto, K. Yamamoto and S. Yoshii, "A Primary Epithelioid Hemangioendothelioma of the Right Atrium: Report of a Case and Literature Review," Open Journal of Thoracic Surgery, Vol. 3 No. 2, 2013, pp. 63-67. doi: 10.4236/ojts.2013.32013.

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