Concurrence of composite adrenal pheochromocytoma-ganglioneuroma and renal pelvic cancer: A case report

Kuniyasu Muraoka, Masashi Honda, Bunya Kawamoto, Seiya Inoue, Katsuya Hikita, Nobuyuki Hinata, Atushi Takenaka

Department of Surgery Related, Division of Urology, Kobe University Graduate School of Medicine, Kobe, Japan.
Department of Surgery, Division of Urology, Tottori University Faculty of Medicine, Yonago, Japan.

DOI: 10.4236/crcm.2013.21025                

Abstract

Embryologically, chromaffin cells of the pheo-chromocytoma and ganglion cells of the ganglioneuroma are both derived from neural crest cells. Composite pheochromocytoma-ganglioneuroma (Pheo-GN) in a single adrenal gland is very rare. A case report of a patient with composite Pheo-GN of the adrenal gland and renal pelvic cancer is presented. Laparoscopic left adrenalectomy, nephroureterectomy and para-aortic lymphadenectomy were performed. This represents the first report of simultaneous surgical treatment for composite Pheo-GN and renal pelvic cancer.

Keywords

Pheochromocytoma; Ganglioneuroma; Renal Pelvic Cancer

Conflicts of Interest

The authors declare no conflicts of interest.

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