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Dyke Davidhoff Masson Syndrome Presenting in Adulthood: A Case Report

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DOI: 10.4236/ojcd.2015.52008    2,912 Downloads   3,182 Views  

ABSTRACT

Dyke Davidhoff Masson syndrome (DDMS) was first described by Dyke Davidhoff and Masson in 1933 in a series of 9 patients [1]. It’s a very rare condition presenting in childhood ranging from infancy to late adolescence [2]. It is characterised by cerebral hemiatrophy, unilateral ventriculomegaly, calvarial thickening, skull and facial asymmetry, sometimes even contralateral hemiplegia in childhood and seizures [2]. An adult presentation is seen in late adolescence or teen age. However in literature the latest presentation reported so far is at 19 years of age [3]. We report a case of Dyke Davidhoff Masson syndrome who presented first time at the age of 28 years which is probably the oldest presentation of this rare entity reported in the literature.

Conflicts of Interest

The authors declare no conflicts of interest.

Cite this paper

Jawanjal, M. , Walke, N. , Bhate, A. and Jawanjal, A. (2015) Dyke Davidhoff Masson Syndrome Presenting in Adulthood: A Case Report. Open Journal of Clinical Diagnostics, 5, 46-49. doi: 10.4236/ojcd.2015.52008.

References

[1] Dyke, C.G., Davidoff, L.M. and Masson, C.B. (1933) Cerebral Hemiatrophy with Homolateral Hypertrophy of the Skull and Sinuses. Surgery, Gynecology & Obstetrics, 57, 588-600.
[2] Koirala, et al. (2012) Dyke Davidhoff Masson Syndrome. Journal of Nobel Medical College, 1, 84-86.
[3] Zilkha, A. (1980) CT of Cerebral Hemiatrophy. American Journal of Roentgenology, 135, 259-562.
http://dx.doi.org/10.2214/ajr.135.2.259
[4] Singh, P., Saggar, K. and Ahluwalia, A. (2010) Dyke-Davidoff-Masson Syndrome: Classical Imaging Findings. Journal of Pediatric Neurosciences, 5, 124-125.
http://dx.doi.org/10.4103/1817-1745.76108
[5] Unal, O., Tombul, T., Cyrak, B., Anlar, O., Incesu, L. and Kayan, M. (2004) Left Hemisphere and Sex Dominance of Cerebral Hemiatrophy (Dyke-Davidoff-Masson Syndrome). Clinical Imaging, 28, 163-165.
http://dx.doi.org/10.1016/S0899-7071(03)00158-X
[6] Pressler, R.M., Binnie, C., Cooper, R. and Robinson, R. (2007) Neonatal and Paediatric Clinical Neurophisiology. Churchill Livingstone Elsevier, Amsterdam, 111-154.
[7] Solomon, G.E., Hilal, S.K., Gold, A.P. and Carpter, S. (1970) Natural History of Acute Hemiplegia of Childhood. Brain, 93, 107-120.
http://dx.doi.org/10.1093/brain/93.1.107

  
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