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Dyke Davidhoff Masson Syndrome Presenting in Adulthood: A Case Report

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DOI: 10.4236/ojcd.2015.52008    2,997 Downloads   3,284 Views  


Dyke Davidhoff Masson syndrome (DDMS) was first described by Dyke Davidhoff and Masson in 1933 in a series of 9 patients [1]. It’s a very rare condition presenting in childhood ranging from infancy to late adolescence [2]. It is characterised by cerebral hemiatrophy, unilateral ventriculomegaly, calvarial thickening, skull and facial asymmetry, sometimes even contralateral hemiplegia in childhood and seizures [2]. An adult presentation is seen in late adolescence or teen age. However in literature the latest presentation reported so far is at 19 years of age [3]. We report a case of Dyke Davidhoff Masson syndrome who presented first time at the age of 28 years which is probably the oldest presentation of this rare entity reported in the literature.

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The authors declare no conflicts of interest.

Cite this paper

Jawanjal, M. , Walke, N. , Bhate, A. and Jawanjal, A. (2015) Dyke Davidhoff Masson Syndrome Presenting in Adulthood: A Case Report. Open Journal of Clinical Diagnostics, 5, 46-49. doi: 10.4236/ojcd.2015.52008.


[1] Dyke, C.G., Davidoff, L.M. and Masson, C.B. (1933) Cerebral Hemiatrophy with Homolateral Hypertrophy of the Skull and Sinuses. Surgery, Gynecology & Obstetrics, 57, 588-600.
[2] Koirala, et al. (2012) Dyke Davidhoff Masson Syndrome. Journal of Nobel Medical College, 1, 84-86.
[3] Zilkha, A. (1980) CT of Cerebral Hemiatrophy. American Journal of Roentgenology, 135, 259-562.
[4] Singh, P., Saggar, K. and Ahluwalia, A. (2010) Dyke-Davidoff-Masson Syndrome: Classical Imaging Findings. Journal of Pediatric Neurosciences, 5, 124-125.
[5] Unal, O., Tombul, T., Cyrak, B., Anlar, O., Incesu, L. and Kayan, M. (2004) Left Hemisphere and Sex Dominance of Cerebral Hemiatrophy (Dyke-Davidoff-Masson Syndrome). Clinical Imaging, 28, 163-165.
[6] Pressler, R.M., Binnie, C., Cooper, R. and Robinson, R. (2007) Neonatal and Paediatric Clinical Neurophisiology. Churchill Livingstone Elsevier, Amsterdam, 111-154.
[7] Solomon, G.E., Hilal, S.K., Gold, A.P. and Carpter, S. (1970) Natural History of Acute Hemiplegia of Childhood. Brain, 93, 107-120.

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