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Sporadic Creutzfeldt-Jakob Disease Presenting with Visual Disturbance—A Case Report in China

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DOI: 10.4236/ijcm.2013.47057    2,880 Downloads   4,361 Views   Citations

ABSTRACT

Creutzfeldt-Jakob disease (CJD) is a rare but fatal neurodegenerative prion disease. Classic CJD comprises a clinical triad of rapidly progressive dementia, myoclonus, and EEG abnormality. At initial presentation, this classic triad is present only in a minority of cases. Visual impairment is one of the predominant manifestations in the course of CJD, especially in Heidenhain variant phenotype. We reported a case presenting with progressive blurred vision, along with other neurological symptoms, who diagnosed as sporadic CJD with cortical blindness in China.

Conflicts of Interest

The authors declare no conflicts of interest.

Cite this paper

G. Tian, L. Sun, Y. He and X. Zhang, "Sporadic Creutzfeldt-Jakob Disease Presenting with Visual Disturbance—A Case Report in China," International Journal of Clinical Medicine, Vol. 4 No. 7, 2013, pp. 321-324. doi: 10.4236/ijcm.2013.47057.

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