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Desmoplastic small round cell tumor of the abdomen: A case report and literature review of therapeutic options

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DOI: 10.4236/health.2012.44031    4,235 Downloads   6,815 Views   Citations

ABSTRACT

Desmoplastic small round cell tumor (DSRCT) is a rare and highly aggressive variety of sarcoma arising typically from abdominal or pelvic peritoneum. Diagnosis and treatment approaches of this entity are complex and require a skilled, experienced, multidisciplinary team. Authors report their experience with a case of an intraabdominal DSRCT arising in a 37-year-old young man in order to discuss the clinico-pathological and radiological behavior of this tumor and underline diagnostic and therapeutic difficulties.

Conflicts of Interest

The authors declare no conflicts of interest.

Cite this paper

Benhammane, H. , Chbani, L. , Ousadden, A. , Mouquit, O. , Tizniti, S. , Amarti, A. , Mellas, N. and Mesbahi, O. (2012) Desmoplastic small round cell tumor of the abdomen: A case report and literature review of therapeutic options. Health, 4, 207-211. doi: 10.4236/health.2012.44031.

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