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Thymic langerhans cell histiocytosis in children: A case report

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DOI: 10.4236/ojped.2012.24052    4,412 Downloads   6,679 Views   Citations

ABSTRACT

Langerhans cell histiocytosis has long been described as a rare systemic disorder involving the proliferation of Langerhans cells with formation of granuloma. The disease may be localised or diffuse. Typical forms of the disease involving the bone, the skin or the pituitary gland have been well described whereas others, such as thymic histiocytosis, are still poorly understood. Here, we report a case of isolated Langerhans cell histiocytosis of the thymus in an infant with non-specific symptoms. We provide a description of the disease and discuss patient management.

Conflicts of Interest

The authors declare no conflicts of interest.

Cite this paper

Poncelet, M. , Chabert, C. , Pierre Pracros, J. and Marec Berard, P. (2012) Thymic langerhans cell histiocytosis in children: A case report. Open Journal of Pediatrics, 2, 303-305. doi: 10.4236/ojped.2012.24052.

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