Author(s)

Antoine Séraphin Gbenou¹, Beaudelaire Romulus Assan^1*, Joseph Akodjenou², Nicole Tchiakpe Enianloko³, Monsoïa Gildas Yasségoungbé¹, Michel Armand Fiogbe⁴

¹Pediatric Surgery Department, University Hospital of Mother and Child Lagune, Cotonou, Benin.
²Anaethesiology and Resuscitation Department, University Hospital of Mother and Child Lagune, Cotonou, Benin.
³Neonatal Department, University Hospital of Mother and Child Lagune, Cotonou, Benin.
⁴University Clinic of Pediatric Surgery CNHU-HKM, Cotonou, Benin.

Introduction: OEIS syndrome, the most severe form of exstrophy-epispadias complex, is characterized by the existence of an omphalocele, a bladder exstrophy, an anal imperforation and a spina bifida. Case Presentation: Two clinical cases admitted at the first day of life in neonatology department are reported; one was born by caesarean section, weighing 2500 g and the other one vaginally with a weight at 1890 g. The first child’s mother was a primigravid, primiparous and the second mother was multiparous. Prenatal ultrasound was performed in one case. The clinical examination found two exstrophied hemi-bladders with two productive ureteral meatus, separated by a double intestinal orifice, a manifestation of anal imperforation, omphalocele, spina bifida and lumbar vertebral malformations; which corresponds to a typical form of OEIS syndrome. One of the babies had an associated clubfoot. The karyotype could not be performed. Both were dead; the first in the early postoperative period, the second one at 16 days of life without surgery. Conclusion: OEIS syndrome is a rare condition and represents a therapeutic challenge in developing countries. Promoting prenatal diagnosis is essential.

OEIS Syndrome, Cloacal Exstrophy, Newborn, Prenatal Diagnosis

Gbenou, A. , Assan, B. , Akodjenou, J. , Enianloko, N. , Yasségoungbé, M. and Fiogbe, M. (2020) Oeis Syndrome (Cloacal Exstrophy): About Two Cases Treated at the Mother and Child Teaching Hospital in Cotonou (Benin). Open Journal of Pediatrics, 10, 535-541. doi: 10.4236/ojped.2020.103054.