Immunosuppressive therapy in idiopathic multifocal fibrosis. A case report

Damian Franzen, Hans-Georg Brochhagen, Effim Benenson

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DOI: 10.4236/ojim.2011.12004                

Abstract

Multifocal fibrosis is a rare condition occurring at any age and characterized by chronic inflammation, soft tissue proliferation and subsequent fibrosis of various vascular connective tissues. Following diagnosis in a 43-year accountant with multiple vascular lesions, the patients was treated successfully with azathioprine and steroids over a period of 3 years. Fatigue and sweating, serologic sign of inflammation and radiological imaging studies normalized completely. Twenty four months after termination of therapy, there were no clinical or serologic signs of relapse.

Keywords

Periaortitis; Multifocal Fibrosis; Retroperitoneal Fibrosis

Conflicts of Interest

The authors declare no conflicts of interest.

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