Syed Ghulam Shabbir (1923-2002) and His Syndrome

Khalid Al Aboud, Daifullah Al Aboud

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DOI: 10.4236/jcdsa.2011.12007                

Abstract

Professor Syed Ghulam Shabbir (1923-2002), is one of the Pakistani well-known dermatologists. In 1986, Shabbir and his colleagues described a novel autosomal recessive syndrome, which they called laryngoonychocutaneous syndrome. They reported this condition, in 22 patients in 12 families living in Lahore, Pakistan. This syndrome is characterized by cutaneous erosions, nail dystrophy and exuberant vascular granulation tissue in certain epithelia, especially conjunctiva and larynx. This report sheds light on Shabbir and the syndrome that bears his name.

Keywords

Laryngo Onycho Cutaneous Syndrome, Shabbir Syndrome, Genodermatoses

Conflicts of Interest

The authors declare no conflicts of interest.

References

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