IgG4-Related Disease Presenting as a Soft Tissue Tumor Affecting Skeletal Muscle: A Case Report ()
David Sáez Martínez,
Felipe López Oliva,
María Jesús Fernández Aceñero,
Elena Fontoira Moyer,
Juan Luis Arranz Cozar
Oncology Department, Fundación Jiménez Díaz, Mad- rid, Spain.
Ortrhopedic Surgery Department, Fundación Jiménez Díaz, Madrid, Spain.
Pathology Department, Fundación Jiménez Díaz, Mad- rid, Spain.
Radiology Department, Fundación Jiménez Díaz, Madrid, Spain.
DOI: 10.4236/ijcm.2013.412A1001
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Abstract
Background: IgG4-related disease is a systemic lymphoproliferative syndrome that shows
IgG4-producing plasma cell expansion in affected organs with fibrotic or
sclerotic changes. The lacrimal glands, salivary glands and pancreas are
typically affected. We report a case of IgG4-related disease presenting a soft
tissue tumor affecting skeletal muscle. Case Report: A 32-year-old man presented a soft tissue mass
in his left arm. Magnetic resonance imaging revealed a spindle like, peripheral
mass, in the lateral head of the triceps of his left arm. Tru-Cut Biopsy
provided the diagnosis of IgG4-related disease affecting skeletal muscle.
Glucocorticoid treatment was effective. Conclusion: To our knowledge, this is the first reported case of IgG4-related disease
affecting skeletal muscle and presenting a soft tissue mass.
Share and Cite:
D. Martínez, F. Oliva, M. Fernández Aceñero, E. Moyer and J. Arranz Cozar, "IgG4-Related Disease Presenting as a Soft Tissue Tumor Affecting Skeletal Muscle: A Case Report,"
International Journal of Clinical Medicine, Vol. 4 No. 12A, 2013, pp. 1-4. doi:
10.4236/ijcm.2013.412A1001.
Conflicts of Interest
The authors declare no conflicts of interest.
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