Anesthetic Management of a Patient with Hermansky-Pudlak Syndrome - Open Journal of Anesthesiology

OJAnes > Vol.5 No.2, February 2015

Open Journal of Anesthesiology

Volume 5, Issue 2 (February 2015)

ISSN Print: 2164-5531 ISSN Online: 2164-5558

Google-based Impact Factor: 0.23 Citations

Anesthetic Management of a Patient with Hermansky-Pudlak Syndrome ()

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DOI: 10.4236/ojanes.2015.52007 4,506 Downloads 5,697 Views Citations

Author(s)

Kelly Zach, Lopa Misra

Affiliation(s)

Mayo Clinic Hospital, Phoenix, AZ, USA.

ABSTRACT

Hermansky-Pudlak Syndrome (HPS) is a rare genetic condition characterized by platelet function abnormalities and oculocutaneous albinism. Other systemic manifestations of the disease include pulmonary fibrosis, granulomatous colitis, impaired renal function, and cardiomyopathy. Due to the systemic extent of the disease, HPS has multiple anesthetic concerns and requires a detailed preoperative evaluation and close perioperative monitoring.

KEYWORDS

Hermanksy-Pudlak, Anesthesia

Share and Cite:

Zach, K. and Misra, L. (2015) Anesthetic Management of a Patient with Hermansky-Pudlak Syndrome. Open Journal of Anesthesiology, 5, 33-36. doi: 10.4236/ojanes.2015.52007.

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